Kyriakopoulou, Maria and Decaux, Guy and El Mourad, Mike and Casado Arroyo, Ruben (2016) Acute Cardiac Tamponade in a 77-year-old Italian Woman with Erdheim-Chester Disease. European Journal of Case Reports in Internal Medicine, 3 (7). ISSN 2284-2594
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Abstract
Erdheim-Chester disease (ECD) is a non-Langerhans’ histiocytosis and a very rare multisystemic disease of unknown aetiology, with skeletal involvement of the long bones and in more than 50% of cases with extraskeletal involvement. The disease was described in 1930 by the anatomopathologist Jakob Erdheim and his student William Chester. More than 500 cases have since been reported. We report the case of a 77-year-old Italian woman with ECD who was admitted to hospital for acute cardiac tamponade. The patient presented with simultaneous cutaneous, retro-orbital, skeletal, cerebral and cardiovascular manifestations and was successfully treated with corticosteroids followed by interferon.
| Item Type: | Article |
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| Uncontrolled Keywords: | Erdheim-Chester disease, tamponade, BRAF, interferon alpha |
| Subjects: | 600 Tecnologia - Scienze applicate > 610 Medicina e salute (Classificare qui la tecnologia dei servizi medici) > 616 Malattie (classificare qui la Clinica medica, la medicina basata sull'evidenza, la Medicina interna, la Medicina sperimentale) |
| Depositing User: | Chiara D'Arpa |
| Date Deposited: | 12 Dec 2016 14:27 |
| Last Modified: | 12 Dec 2016 14:27 |
| URI: | http://eprints.bice.rm.cnr.it/id/eprint/15737 |
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