Oliveira, Margarida and Monteiro, Sofia and dos Santos, Joana and Silva, Ana Catarina and Morais Ferreira, Rute (2020) Erdheim-Chester Disease: A Rare Clinical Entity. European Journal of Case Reports in Internal Medicine, 7 (9). pp. 1-4. ISSN ISSN: 2284-2594
|
Text
1630-Article Text-14653-1-10-20200625.pdf - Published Version Download (868kB) | Preview |
Abstract
Pericardial effusion represents a diagnostic challenge. Erdheim-Chester disease (ECD), though a rare cause, should be considered in the differential diagnosis. An 88-year-old woman was admitted to the hospital due to retrosternal pain, dyspnoea and constitutional symptoms. Hypoxaemic respiratory failure and increased inflammatory markers were documented. A chest x-ray revealed an increased cardiothoracic ratio. An echocardiogram showed a moderate-volume pericardial effusion, without signs of cardiac tamponade. A thoraco-abdomino-pelvic CT scan found a bilateral perirenal soft tissue halo. Perirenal mass biopsy showed diffuse infiltration by foamy histiocytes (CD68+), without IgG4, compatible with ECD. The correlation of anamnesis, radiology and histology is crucial for the diagnosis of ECD.
| Item Type: | Article |
|---|---|
| Uncontrolled Keywords: | Erdheim-Chester disease, pericardial effusion, retroperitoneal space |
| Subjects: | 600 Tecnologia - Scienze applicate 600 Tecnologia - Scienze applicate > 610 Medicina e salute (Classificare qui la tecnologia dei servizi medici) 600 Tecnologia - Scienze applicate > 610 Medicina e salute (Classificare qui la tecnologia dei servizi medici) > 616 Malattie (classificare qui la Clinica medica, la medicina basata sull'evidenza, la Medicina interna, la Medicina sperimentale) > 616.8 Malattie del sistema nervoso e disturbi mentali (Classificare qui la Neuropsichiatria, la Neurologia) |
| Depositing User: | Marina Spanti |
| Date Deposited: | 15 Dec 2021 13:19 |
| Last Modified: | 15 Dec 2021 13:19 |
| URI: | http://eprints.bice.rm.cnr.it/id/eprint/21001 |
Actions (login required)
 |
View Item |
